Home Print this page Email this page Users Online: 69
Home About us Editorial board Search Ahead of print Current issue Archives Submit article Instructions Subscribe Contacts Login 
Year : 2013  |  Volume : 20  |  Issue : 2  |  Page : 101-103

Unusual age at presentation of klippel-trenaunay syndrome

1 Department of Radiodiagnosis, Era's Lucknow Medical College, Lucknow, Uttar Pradesh, India
2 Department of Pediatrics, Era's Lucknow Medical College, Lucknow, Uttar Pradesh, India

Correspondence Address:
Sanjeev Singhal
C-19, PG Boys Auditorium Hostel, Era's Lucknow Medical College, Lucknow, Uttar Pradesh - 226 003
Login to access the Email id

Source of Support: None, Conflict of Interest: None

DOI: 10.4103/1115-1474.121102

Rights and Permissions

Klippel-Trenaunay (KT) syndrome is a congenital vascular disorder which is rare and affects one or both limbs. It has incidence of about 2-5 in 100,000. French physicians Klippel and Trenaunay first described this syndrome in the year 1900. They named the syndrome as "nevus vasculosus osteohypertrophicus". In 1907, Park Weber named the same condition hemangiectatic hypertrophy. The etiology is unknown. Though it is a sporadic condition, paradominant inheritance pattern has also been suggested. Patients generally present in the first decade of life. It affects males more than females. KT syndrome is a congenital circulatory disorder typically comprising of the triad cutaneous capillary angioma, bone and soft tissue hypertrophy and varicose veins. There are several theories about its pathogenesis. The management of this syndrome consists mainly of early diagnosis, prevention and treatment of complications. We report the case of a 30-year-old male patient with KT syndrome showing the classical triad.

Print this article     Email this article
 Next article
 Previous article
 Table of Contents

 Similar in PUBMED
   Search Pubmed for
   Search in Google Scholar for
 Related articles
 Citation Manager
 Access Statistics
 Reader Comments
 Email Alert *
 Add to My List *
 * Requires registration (Free)

 Article Access Statistics
    PDF Downloaded16    
    Comments [Add]    

Recommend this journal